Source Code Name Case count Share of cases (%)
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M353) Polymyalgia rheumatica. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 3531
OUTPAT OUTPAT_ICD10(M353) Polymyalgia rheumatica 3336
OUTPAT OUTPAT_ICD10(M350) Sicca syndrome [Sjögren] 2597
INPAT INPAT_ICD10(M353) Polymyalgia rheumatica 1752
OUTPAT OUTPAT_ICD10(M357) Hypermobility syndrome 1522
OUTPAT OUTPAT_ICD10(M359) Systemic involvement of connective tissue, unspecified 1467
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M350) Sicca syndrome [Sjögren]. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 1236
OUTPAT OUTPAT_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica 913
OUTPAT OUTPAT_ICD10(M329) Systemic lupus erythematosus, unspecified 865
INPAT INPAT_ICD10(M350) Sicca syndrome [Sjögren] 802
OUTPAT OUTPAT_ICD10(M351) Other overlap syndromes 537
INPAT INPAT_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica 522
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M357) Hypermobility syndrome. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 492
OUTPAT OUTPAT_ICD10(M313) Wegener's granulomatosis 445
INPAT INPAT_ICD10(M329) Systemic lupus erythematosus, unspecified 430
OUTPAT OUTPAT_ICD10(M341) CR(E)ST syndrome 416
INPAT INPAT_ICD10(M359) Systemic involvement of connective tissue, unspecified 380
INPAT INPAT_ICD10(M313) Wegener's granulomatosis 315
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M329) Systemic lupus erythematosus, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 307
INPAT INPAT_ICD10(M357) Hypermobility syndrome 305
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 303
OUTPAT OUTPAT_ICD10(M349) Systemic sclerosis, unspecified 279
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M359) Systemic involvement of connective tissue, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 266
OUTPAT OUTPAT_ICD10(M321) Systemic lupus erythematosus with organ or system involvement 244
OUTPAT OUTPAT_ICD10(M328) Other forms of systemic lupus erythematosus 235
OUTPAT OUTPAT_ICD10(M332) Polymyositis 215
OUTPAT OUTPAT_ICD10(M319) Necrotizing vasculopathy, unspecified 198
OUTPAT OUTPAT_ICD10(M316) Other giant cell arteritis 185
INPAT INPAT_ICD10(M351) Other overlap syndromes 182
OUTPAT OUTPAT_ICD10(M320) Drug-induced systemic lupus erythematosus 178
INPAT INPAT_ICD9(7100A) Systemic lupus erythematosus 165
OUTPAT OUTPAT_ICD10(M358) Other specified systemic involvement of connective tissue 162
INPAT INPAT_ICD10(M321) Systemic lupus erythematosus with organ or system involvement 158
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M341) CR(E)ST syndrome. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 157
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M313) Wegener's granulomatosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 154
OUTPAT OUTPAT_ICD10(M317) Microscopic polyangiitis 152
OUTPAT OUTPAT_ICD10(M355) Multifocal fibrosclerosis 146
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M351) Other overlap syndromes. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 141
OUTPAT OUTPAT_ICD10(M339) Dermatopolymyositis, unspecified 140
OUTPAT OUTPAT_ICD10(M311) Thrombotic microangiopathy 136
OUTPAT OUTPAT_ICD10(M300) Polyarteritis nodosa 133
OUTPAT OUTPAT_ICD10(M331) Other dermatomyositis 133
INPAT INPAT_ICD10(M341) CR(E)ST syndrome 128
INPAT INPAT_ICD10(M332) Polymyositis 124
INPAT INPAT_ICD10(M319) Necrotizing vasculopathy, unspecified 123
OUTPAT OUTPAT_ICD10(M340) Progressive systemic sclerosis 117
OUTPAT OUTPAT_ICD10(M310) Hypersensitivity angiitis 104
OUTPAT OUTPAT_ICD10(M301) Polyarteritis with lung involvement [Churg-Strauss] 102
OUTPAT OUTPAT_ICD10(M318) Other specified necrotizing vasculopathies 102
INPAT INPAT_ICD9(7250A) Polymyalgia rheumatica 100
INPAT INPAT_ICD10(M300) Polyarteritis nodosa 97
INPAT INPAT_ICD10(M316) Other giant cell arteritis 96
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M32) Systemic lupus erythematosus. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 93
INPAT INPAT_ICD10(M328) Other forms of systemic lupus erythematosus 88
INPAT INPAT_ICD10(M317) Microscopic polyangiitis 87
INPAT INPAT_ICD10(M311) Thrombotic microangiopathy 85
INPAT INPAT_ICD10(M349) Systemic sclerosis, unspecified 84
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M349) Systemic sclerosis, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 84
OUTPAT OUTPAT_ICD10(M352) Behçet's disease 83
INPAT INPAT_ICD9(7102B) Diffuse diseases of connective tissue, Sicca syndrome 81
INPAT INPAT_ICD10(M339) Dermatopolymyositis, unspecified 80
OUTPAT OUTPAT_ICD10(M348) Other forms of systemic sclerosis 79
INPAT INPAT_ICD8(73491) Diffuse diseases of connective tissue, Collagenosis NUD 78
INPAT INPAT_ICD9(7109X) Unspecified diffuse connective tissue disease 70
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M332) Polymyositis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 70
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M316) Other giant cell arteritis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 65
INPAT INPAT_ICD10(M310) Hypersensitivity angiitis 63
INPAT INPAT_ICD10(M320) Drug-induced systemic lupus erythematosus 63
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M328) Other forms of systemic lupus erythematosus. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 60
INPAT INPAT_ICD9(7102A) Diffuse diseases of connective tissue, Sicca syndrome 59
OUTPAT OUTPAT_ICD10(M308) Other conditions related to polyarteritis nodosa 58
INPAT INPAT_ICD10(M331) Other dermatomyositis 56
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M35) Other systemic involvement of connective tissue. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 55
INPAT INPAT_ICD10(M301) Polyarteritis with lung involvement [Churg-Strauss] 54
INPAT INPAT_ICD10(M318) Other specified necrotizing vasculopathies 51
INPAT INPAT_ICD9(4476A) Arteritis, unspecified 51
OUTPAT OUTPAT_ICD10(M32) Systemic lupus erythematosus 51
INPAT INPAT_ICD10(M340) Progressive systemic sclerosis 48
OUTPAT OUTPAT_ICD10(M314) Aortic arch syndrome [Takayasu] 48
INPAT INPAT_ICD10(M308) Other conditions related to polyarteritis nodosa 47
INPAT INPAT_ICD10(M355) Multifocal fibrosclerosis 46
OUTPAT OUTPAT_ICD10(M354) Diffuse (eosinophilic) fasciitis 41
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M321) Systemic lupus erythematosus with organ or system involvement. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 40
INPAT INPAT_ICD10(M358) Other specified systemic involvement of connective tissue 39
OUTPAT OUTPAT_ICD10(M303) Mucocutaneous lymph node syndrome [Kawasaki] 37
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M339) Dermatopolymyositis, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 37
INPAT INPAT_ICD10(M348) Other forms of systemic sclerosis 36
INPAT INPAT_ICD10(M303) Mucocutaneous lymph node syndrome [Kawasaki] 35
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M358) Other specified systemic involvement of connective tissue. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 34
OUTPAT OUTPAT_ICD10(M330) Juvenile dermatomyositis 33
DEATH DEATH_ICD10(M353) Polymyalgia rheumatica 31
INPAT INPAT_ICD8(73490) Diffuse diseases of connective tissue, Keratoconjunctivitis sicca (dry eye disease). Sjögren's syndrome 31
INPAT INPAT_ICD8(44698) Polyarteritis nodosa and allied conditions, Other 30
INPAT INPAT_ICD9(7108X) Other specified diffuse diseases of connective tissue 30
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M317) Microscopic polyangiitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 30
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M34) Systemic sclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 30
INPAT INPAT_ICD10(M352) Behçet's disease 29
OUTPAT OUTPAT_ICD10(M364) Arthropathy in hypersensitivity reactions classified elsewhere 29
DEATH DEATH_ICD10(M313) Wegener's granulomatosis 28
INPAT INPAT_ICD10(M314) Aortic arch syndrome [Takayasu] 28
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M319) Necrotizing vasculopathy, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 28
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M331) Other dermatomyositis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 27
INPAT INPAT_ICD9(4462A) Hypersensitivity angiitis 26
INPAT INPAT_ICD9(4461A) Acute febrile mucocutaneous lymph node syndrome [MCLS] 25
OUTPAT OUTPAT_ICD10(M35) Other systemic involvement of connective tissue 25
OUTPAT OUTPAT_ICD10(M368) Systemic disorders of connective tissue in other diseases classified elsewhere 25
OUTPAT OUTPAT_ICD10(M362) Haemophilic arthropathy (D66-D68+) 24
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M300) Polyarteritis nodosa. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 23
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M301) Polyarteritis with lung involvement [Churg-Strauss]. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 23
INPAT INPAT_ICD8(73498) Diffuse diseases of connective tissue, Alii definiti 21
INPAT INPAT_ICD9(4464A) Wegener's granulomatosis 21
INPAT INPAT_ICD9(4465A) Giant cell arteritis 21
INPAT INPAT_ICD9(7101A) Diffuse diseases of connective tissue, Systemic sclerosis 20
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M352) Behçet's disease. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 20
INPAT INPAT_ICD8(71610) Polymyositis and dermatomyositis, Polymyositis 19
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M348) Other forms of systemic sclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 19
INPAT INPAT_ICD10(M330) Juvenile dermatomyositis 18
INPAT INPAT_ICD10(M354) Diffuse (eosinophilic) fasciitis 18
INPAT INPAT_ICD8(44638) Polyarteritis nodosa and allied conditions, Polymyalgia arteritica (rheumatica) 18
INPAT INPAT_ICD9(7104A) Polymyositis 18
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M340) Progressive systemic sclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 18
INPAT INPAT_ICD8(73499) Diffuse diseases of connective tissue, Other and unspecified 16
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M314) Aortic arch syndrome [Takayasu]. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 16
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M355) Multifocal fibrosclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 16
OUTPAT OUTPAT_ICD10(M312) Lethal midline granuloma 15
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M354) Diffuse (eosinophilic) fasciitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 15
DEATH DEATH_ICD10(M332) Polymyositis 14
DEATH DEATH_ICD10(M350) Sicca syndrome [Sjögren] 14
OUTPAT OUTPAT_ICD10(M361) Arthropathy in neoplastic disease (C00-D48+) 14
INPAT INPAT_ICD9(4460A) Polyarteritis nodosa and allied conditions, Polyarteritis nodosa 13
DEATH DEATH_ICD10(M329) Systemic lupus erythematosus, unspecified 12
DEATH DEATH_ICD10(M341) CR(E)ST syndrome 12
INPAT INPAT_ICD10(M362) Haemophilic arthropathy (D66-D68+) 12
INPAT INPAT_ICD10(M364) Arthropathy in hypersensitivity reactions classified elsewhere 12
INPAT INPAT_ICD8(71600) Polymyositis and dermatomyositis, Dermatomyositis 12
INPAT INPAT_ICD9(7103B) Diffuse diseases of connective tissue, Dermatomyositis 12
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M310) Hypersensitivity angiitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 12
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M318) Other specified necrotizing vasculopathies. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 12
DEATH DEATH_ICD10(M359) Systemic involvement of connective tissue, unspecified 11
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M30) Polyarteritis nodosa and related conditions. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 11
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M364) Arthropathy in hypersensitivity reactions classified elsewhere. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 11
INPAT INPAT_ICD10(M368) Systemic disorders of connective tissue in other diseases classified elsewhere 10
INPAT INPAT_ICD8(73409) Diffuse diseases of connective tissue, Sclerosis systematica NUD 10
OUTPAT OUTPAT_ICD10(M356) Relapsing panniculitis [Weber-Christian] 10
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M308) Other conditions related to polyarteritis nodosa. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 10
DEATH DEATH_ICD10(M317) Microscopic polyangiitis 9
INPAT INPAT_ICD10(M361) Arthropathy in neoplastic disease (C00-D48+) 9
INPAT INPAT_ICD8(44600) Polyarteritis nodosa and allied conditions, Polyarteritis nodosa 9
INPAT INPAT_ICD8(44630) Polyarteritis nodosa and allied conditions, Arteritis cranialis (temporalis) 9
OUTPAT OUTPAT_ICD10(M34) Systemic sclerosis 9
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M311) Thrombotic microangiopathy. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 9
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M33) Dermatopolymyositis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 9
INPAT INPAT_ICD9(7103A) Diffuse diseases of connective tissue, Dermatomyositis 8
INPAT INPAT_ICD8(74310) Other congenital anomalies of nervous system, Microcephalus 7
INPAT INPAT_ICD9(4466A) Thrombotic microangiopathy 7
INPAT INPAT_ICD9(4467A) Takayasu's disease 7
OUTPAT OUTPAT_ICD10(M342) Systemic sclerosis induced by drugs and chemicals 7
OUTPAT OUTPAT_ICD10(M360) Dermato(poly)myositis in neoplastic disease (C00-D48+) 7
DEATH DEATH_ICD10(M300) Polyarteritis nodosa 6
DEATH DEATH_ICD10(M331) Other dermatomyositis 6
INPAT INPAT_ICD10(M312) Lethal midline granuloma 6
INPAT INPAT_ICD8(73401) Diffuse diseases of connective tissue, Sclerosis systematica acrosclerotica 6
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M320) Drug-induced systemic lupus erythematosus. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 6
DEATH DEATH_ICD10(M311) Thrombotic microangiopathy 5
DEATH DEATH_ICD10(M319) Necrotizing vasculopathy, unspecified 5
DEATH DEATH_ICD10(M349) Systemic sclerosis, unspecified 5
INPAT INPAT_ICD8(44620) Polyarteritis nodosa and allied conditions, Other hypersensitivity angiitis 5
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M362) Haemophilic arthropathy (D66-D68+). Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 5