Source Code Name Case count Share of cases (%)
OUTPAT OUTPAT_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica 913
INPAT INPAT_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica 522
OUTPAT OUTPAT_ICD10(M313) Wegener's granulomatosis 445
INPAT INPAT_ICD10(M313) Wegener's granulomatosis 315
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 303
OUTPAT OUTPAT_ICD10(M319) Necrotizing vasculopathy, unspecified 198
OUTPAT OUTPAT_ICD10(M316) Other giant cell arteritis 185
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M313) Wegener's granulomatosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 154
OUTPAT OUTPAT_ICD10(M317) Microscopic polyangiitis 152
OUTPAT OUTPAT_ICD10(M311) Thrombotic microangiopathy 136
INPAT INPAT_ICD10(M319) Necrotizing vasculopathy, unspecified 123
OUTPAT OUTPAT_ICD10(M310) Hypersensitivity angiitis 104
OUTPAT OUTPAT_ICD10(M318) Other specified necrotizing vasculopathies 102
INPAT INPAT_ICD10(M316) Other giant cell arteritis 96
INPAT INPAT_ICD10(M317) Microscopic polyangiitis 87
INPAT INPAT_ICD10(M311) Thrombotic microangiopathy 85
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M316) Other giant cell arteritis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 65
INPAT INPAT_ICD10(M310) Hypersensitivity angiitis 63
INPAT INPAT_ICD10(M318) Other specified necrotizing vasculopathies 51
INPAT INPAT_ICD9(4476A) Arteritis, unspecified 51
OUTPAT OUTPAT_ICD10(M314) Aortic arch syndrome [Takayasu] 48
INPAT INPAT_ICD8(44698) Polyarteritis nodosa and allied conditions, Other 30
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M317) Microscopic polyangiitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 30
DEATH DEATH_ICD10(M313) Wegener's granulomatosis 28
INPAT INPAT_ICD10(M314) Aortic arch syndrome [Takayasu] 28
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M319) Necrotizing vasculopathy, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 28
INPAT INPAT_ICD9(4462A) Hypersensitivity angiitis 26
INPAT INPAT_ICD9(4464A) Wegener's granulomatosis 21
INPAT INPAT_ICD9(4465A) Giant cell arteritis 21
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M314) Aortic arch syndrome [Takayasu]. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 16
OUTPAT OUTPAT_ICD10(M312) Lethal midline granuloma 15
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M310) Hypersensitivity angiitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 12
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M318) Other specified necrotizing vasculopathies. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 12
DEATH DEATH_ICD10(M317) Microscopic polyangiitis 9
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M311) Thrombotic microangiopathy. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 9
INPAT INPAT_ICD9(4466A) Thrombotic microangiopathy 7
INPAT INPAT_ICD9(4467A) Takayasu's disease 7
INPAT INPAT_ICD10(M312) Lethal midline granuloma 6
DEATH DEATH_ICD10(M311) Thrombotic microangiopathy 5
DEATH DEATH_ICD10(M319) Necrotizing vasculopathy, unspecified 5
INPAT INPAT_ICD8(44620) Polyarteritis nodosa and allied conditions, Other hypersensitivity angiitis 5