| Source | Code | Name | Case count | Share of cases (%) |
|---|---|---|---|---|
| OUTPAT | OUTPAT_ICD10(G122) | Motor neuron disease | 475 | |
| INPAT | INPAT_ICD10(G122) | Motor neuron disease | 377 | |
| DEATH | DEATH_ICD10(G122) | Motor neuron disease | 239 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(G122) | Motor neuron disease. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 185 | |
| OUTPAT | OUTPAT_ICD10(G119) | Hereditary ataxia, unspecified | 160 | |
| OUTPAT | OUTPAT_ICD10(G129) | Spinal muscular atrophy, unspecified | 98 | |
| OUTPAT | OUTPAT_ICD10(G112) | Late-onset cerebellar ataxia | 80 | |
| INPAT | INPAT_ICD10(G119) | Hereditary ataxia, unspecified | 74 | |
| OUTPAT | OUTPAT_ICD10(G128) | Other spinal muscular atrophies and related syndromes | 72 | |
| OUTPAT | OUTPAT_ICD10(G118) | Other hereditary ataxias | 47 | |
| OUTPAT | OUTPAT_ICD10(G121) | Other inherited spinal muscular atrophy | 45 | |
| OUTPAT | OUTPAT_ICD10(G114) | Hereditary spastic paraplegia | 36 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(G119) | Hereditary ataxia, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 35 | |
| INPAT | INPAT_ICD10(G129) | Spinal muscular atrophy, unspecified | 34 | |
| OUTPAT | OUTPAT_ICD10(G10) | Huntington's disease | 29 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(G129) | Spinal muscular atrophy, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 29 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(G112) | Late-onset cerebellar ataxia. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 27 | |
| INPAT | INPAT_ICD10(G121) | Other inherited spinal muscular atrophy | 26 | |
| INPAT | INPAT_ICD10(G112) | Late-onset cerebellar ataxia | 25 | |
| INPAT | INPAT_ICD10(G118) | Other hereditary ataxias | 20 | |
| INPAT | INPAT_ICD10(G128) | Other spinal muscular atrophies and related syndromes | 19 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(G121) | Other inherited spinal muscular atrophy. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 19 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(G128) | Other spinal muscular atrophies and related syndromes. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 19 | |
| INPAT | INPAT_ICD10(G114) | Hereditary spastic paraplegia | 15 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(G114) | Hereditary spastic paraplegia. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 15 | |
| INPAT | INPAT_ICD10(G10) | Huntington's disease | 14 | |
| OUTPAT | OUTPAT_ICD10(G130) | Paraneoplastic neuromyopathy and neuropathy | 14 | |
| OUTPAT | OUTPAT_ICD10(G1100) | Cerebellar dysplasia and aplasia | 12 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(G1102) | Dysequilibrium syndrome. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 12 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(G118) | Other hereditary ataxias. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 12 | |
| OUTPAT | OUTPAT_ICD10(G120) | Infantile spinal muscular atrophy, type I [Werdnig-Hoffman] | 11 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(G10) | Huntington's disease. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 10 | |
| INPAT | INPAT_ICD10(G130) | Paraneoplastic neuromyopathy and neuropathy | 8 | |
| OUTPAT | OUTPAT_ICD10(G1118) | Early-onset cerebellar ataxia | 8 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(G11) | Hereditary ataxia. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 7 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(G1118) | Early-onset cerebellar ataxia. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 6 | |
| INPAT | INPAT_ICD10(G1118) | Early-onset cerebellar ataxia | 5 | |
| INPAT | INPAT_ICD10(G120) | Infantile spinal muscular atrophy, type I [Werdnig-Hoffman] | 5 |